Assuntos
Dextrocardia/complicações , Aneurisma Cardíaco/etiologia , Comunicação Interventricular/complicações , Estenose Subvalvar Pulmonar/etiologia , Valva Pulmonar , Transposição dos Grandes Vasos/complicações , Procedimentos Cirúrgicos Cardíacos , Pré-Escolar , Cineangiografia , Transposição das Grandes Artérias Corrigida Congenitamente , Dextrocardia/diagnóstico , Ecocardiografia Doppler em Cores , Aneurisma Cardíaco/diagnóstico , Aneurisma Cardíaco/fisiopatologia , Aneurisma Cardíaco/cirurgia , Comunicação Interventricular/diagnóstico , Comunicação Interventricular/fisiopatologia , Comunicação Interventricular/cirurgia , Humanos , Masculino , Estenose Subvalvar Pulmonar/diagnóstico , Estenose Subvalvar Pulmonar/fisiopatologia , Valva Pulmonar/diagnóstico por imagem , Valva Pulmonar/fisiopatologia , Transposição dos Grandes Vasos/diagnóstico , Resultado do TratamentoRESUMO
OBJECTIVE: Vein of Galen aneurysmal malformations (VGAMs) are rare congenital malformations thought to develop during weeks 6 to 11 of fetal life. Although they represent less than 1% of all cerebral vascular malformations, they constitute up to 30% of all pediatric vascular malformations. Vein of Galen aneurysmal malformations cause high-output heart failure in the fetus and neonate secondary to the decreased resistance and high blood flow in the lesion. We describe 2 cases, 1 prenatal and 1 postnatal, in which unusual aortic Doppler flow patterns and substantial brachiocephalic vessel dilation contributed to the discovery of a VGAM. METHODS: Echocardiographic findings associated with VGAM malformations in 2 cases are described. RESULTS: Unusual Doppler flow patterns and substantial brachiocephalic vessel dilation were seen in both cases. Pseudocoarctation of the aorta was also noted in both cases. CONCLUSIONS: The echocardiographic findings in fetal and neonatal VGAM may include pseudocoarctation of the aorta. Abnormal fetal cardiac findings should raise the practitioner's suspicion for cerebral malformations and vice versa.
